Most common cardiomyopathy and the most frequent cause of sudden cardiac death in young people.
Presentation varies from asymptomatic to symptoms of heart failure.
Physical examination may be normal at rest. Auscultation along the left sternal border when the patient is standing after a brief period of exercise may elicit a murmur.
Family history may be present. Echocardiography should be used to screen first-degree family members.
Has a benign prognosis in the majority of patients.
Medical therapy with beta-blockers, calcium-channel blockers, or disopyramide is used in symptomatic patients.
A subset of patients with increased risk for sudden death should undergo defibrillator implantation.
Long axis echocardiography view - asymmetrical septal hypertrophy
From the personal collection of Dr Anji T. Yetman MD, University of Utah; used with permission